This number of anomalies share a common av junction with abnormalities for the AV valves (separate valves in partial AV septal problem, typical AV valve when you look at the complete type; see Figure 1B). The left AV valve is trileaflet (Figures 1B and 2 B), made up of the mural leaflet additionally the inferior and superior leaflets, that are fused and point toward the remaining ventricular outflow (вЂњ11th hourвЂќ). The exact distance through the remaining AV valve annulus in to the remaining apex that is ventricular appreciably lower than that through the apex into the aortic annulus, whereas generally the two distances are equal. This inlet to outlet disproportion produces theвЂњgooseneck that is characteristicвЂќ which used become a significant diagnostic function on remaining ventriculography. Also, this elongation associated with remaining outflow that is ventricular, combined with proven fact that there are chordal attachments of this remaining AV valve to your ventricular septum within these clients, types the basis for the growth of discrete subaortic obstruction, which could happen even later after effective fix of this problem. 7 The unusual AV junction results within an вЂњunwedgedвЂќ aorta and results in a displacement of this AV conduction muscle, which often creates the characteristic left-axis deviation and predisposes these clients to heart block.
The most frequent connected anomalies certainly are a secundum ASD and a persistent left SVC draining in to the coronary sinus.